Volume : 9, Issue : 6, June - 2020

A RARE COMPLICATION -

Dr. Shaily Panwar, Dr. Shailendra Singh Sengar, Dr. Badrul Qamar, Dr. Pradeep Kumar Sharma

Abstract :

We present an extremely rare case of a young female, having spectrum of tuberous sclerosis complex, exhibiting life threatening Wunderlich’s syndrome after non traumatic rupture of renal angiomyolipoma. The early ultrasound and Computed tomography (CT) aids in the prompt diagnosis of tuberous sclerosis complex, in patients with retroperitoneal hemorrhage of large right renal angiomyolipoma. Patient also have B/L renal angiomyolipomas, hepatic lipomas, calcified subependymal nodules, lung cysts and facial adenoma sebaceum. Patient underwent immediate laparotomy and thereafter was stable and discharged. All the patients of tuberous sclerosis should be screened radiologically for giant renal angiomyolipoma for prompt treatment of life threatening condition of Wunderlich syndrome.